AARS2 | ATP5F1D | COQ9 | DNAJC19 | HADH | MCCC2 | NDUFA13 | PARS2 | SCO1 | TCIRG1 |
AASS | ATP5F1E | COX10 | DNM1L | HADHA | MCEE | NDUFA2 | PC | SCO2 | TFAM |
ABAT | ATP5MD | COX14 | DNM2 | HADHB | MDH2 | NDUFA4 | PCCA | SCP2 | TIMM44 |
ABCB6 | ATP7B | COX15 | EARS2 | HARS2 | MFF | NDUFA6 | PCCB | SDHA | TIMM8A |
ABCB7 | ATPAF2 | COX20 | ECHS1 | HAX1 | MFN2 | NDUFA8 | PCK2 | SDHAF1 | TIMMDC1 |
ABCD1 | AUH | COX4I2 | EHHADH | HCCS | MGME1 | NDUFA9 | PDHA1 | SDHAF2 | TK2 |
ACACA | BAX | COX6A1 | ELAC2 | HIBCH | MICU1 | NDUFAF1 | PDHB | SDHB | TMEM126A |
ACAD8 | BCKDHA | COX6A2 | ETFA | HK1 | MIPEP | NDUFAF2 | PDHX | SDHC | TMEM126B |
ACAD9 | BCKDHB | COX6B1 | ETFB | HLCS | MLYCD | NDUFAF3 | PDK3 | SDHD | TMEM70 |
ACADM | BCKDK | COX7B | ETFDH | HMGCL | MMAA | NDUFAF4 | PDP1 | SERAC1 | TMLHE |
ACADS | BCL2 | COX8A | ETHE1 | HMGCS2 | MMAB | NDUFAF5 | PDSS1 | SFXN4 | TPP1 |
ACADSB | BCS1L | CPOX | FARS2 | HOGA1 | MMACHC | NDUFAF6 | PDSS2 | SLC16A1 | TRIT1 |
ACADVL | BOLA3 | CPS1 | FASTKD2 | HSD17B10 | MMADHC | NDUFAF8 | PDX1 | SLC19A3 | TRMT10C |
ACAT1 | BTD | CPT1A | FBXL4 | HSD3B2 | MOCS1 | NDUFB11 | PET100 | SLC25A1 | TRMT5 |
ACO2 | C12orf65 | CPT1C | FDX2 | HSPA9 | MPC1 | NDUFB3 | PHB | SLC25A12 | TRMU |
ACOX1 | C19orf12 | CPT2 | FDXR | HSPD1 | MPV17 | NDUFB8 | PINK1 | SLC25A13 | TRNT1 |
ACSF3 | C19orf70 | CYB5A | FECH | HTRA2 | MRPL3 | NDUFB9 | PNKD | SLC25A15 | TSFM |
ACSL4 | C1QBP | CYB5R3 | FH | IARS2 | MRPL44 | NDUFS1 | PNPLA8 | SLC25A19 | TTBK2 |
AFG3L2 | CA5A | CYBB | FLAD1 | IBA57 | MRPS14 | NDUFS2 | PNPT1 | SLC25A20 | TTC19 |
AGK | CARS2 | CYC1 | FOXRED1 | IDH2 | MRPS16 | NDUFS3 | POLG | SLC25A22 | TUFM |
AGXT | CASP8 | CYCS | FXN | IDH3B | MRPS2 | NDUFS4 | POLG2 | SLC25A26 | TWNK |
AIFM1 | CAT | CYP11A1 | GARS | ISCA2 | MRPS22 | NDUFS6 | PPM1K | SLC25A3 | TXN2 |
AK2 | CAVIN1 | CYP11B1 | GATM | ISCU | MRPS25 | NDUFS7 | PPOX | SLC25A38 | TXNRD2 |
ALAS2 | CHCHD10 | CYP11B2 | GCDH | IVD | MRPS34 | NDUFS8 | PRODH | SLC25A4 | TYMP |
ALDH18A1 | CHKB | CYP24A1 | GCK | KARS | MRPS7 | NDUFV1 | PTCD3 | SLC25A46 | UCP1 |
ALDH2 | CISD2 | CYP27A1 | GCSH | KIF1B | MSRB3 | NDUFV2 | PTRH2 | SOD1 | UCP3 |
ALDH3A2 | CLN3 | CYP27B1 | GDAP1 | KIF5A | MTFMT | NFU1 | PTS | SOD2 | UNG |
ALDH4A1 | CLPB | D2HGDH | GFER | L2HGDH | MTHFD1 | NNT | PUS1 | SPART | UQCC2 |
ALDH5A1 | CLPP | DARS2 | GFM1 | LARS2 | MTO1 | NTHL1 | PYCR1 | SPG7 | UQCC3 |
ALDH6A1 | COA3 | DBT | GFM2 | LIAS | MTPAP | NUBPL | PYCR2 | SPTLC2 | UQCRB |
ALDH7A1 | COA5 | DECR1 | GK | LIPT1 | MTRR | OAT | QDPR | STAR | UQCRC2 |
AMACR | COA6 | DGUOK | GLDC | LIPT2 | MUT | OGDH | RANBP2 | STOM | UQCRFS1 |
AMT | COASY | DHODH | GLRX5 | LONP1 | MUTYH | OGG1 | RARS2 | SUCLA2 | UQCRQ |
APOPT1 | COQ2 | DHTKD1 | GLUD1 | LRPPRC | NADK2 | OPA1 | REEP1 | SUCLG1 | UROS |
APTX | COQ4 | DIABLO | GLYCTK | LYRM4 | NAGS | OPA3 | RMND1 | SUGCT | VARS2 |
ARMS2 | COQ5 | DLAT | GPD2 | LYRM7 | NARS2 | OTC | RNASEH1 | SUOX | WARS2 |
ASS1 | COQ6 | DLD | GPT2 | MAOA | NDUFA1 | OXCT1 | RNASEL | SURF1 | WDR81 |
ATAD3A | COQ7 | DMGDH | GPX1 | MAOB | NDUFA10 | PAM16 | RRM2B | TACO1 | XPNPEP3 |
ATIC | COQ8A | DMPK | GSR | MARS2 | NDUFA11 | PANK2 | SARDH | TARS2 | YARS2 |
ATP5F1A | COQ8B | DNA2 | GTPBP3 | MCCC1 | NDUFA12 | PARK7 | SARS2 | TAZ | YME1L1 |